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Cutaneous mastocytosis

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Disease definition

A rare group of mastocytosis diseases characterized by abnormal accumulation and proliferation of mast cells in the skin and including the three recognised forms: diffuse cutaneous mastocytosis, cutaneous mastocytoma and, the most common form, maculopapular cutaneous mastocytosis. In some cases (most commonly in adults), cutaneous mastocytosis may occur in association with mast cell infiltration of various extracutaneous organs, in which case the disorder is referred to as systemic mastocytosis.

ORPHA:66646

Classification level: Group of disorders

Prevalence: Unknown

Inheritance: Not applicable

Age of onset: Childhood

ICD-11: 2A21.1

UMLS: C1136033

MeSH: D034701

GARD: 7842

A summary on this disease is available in Français, Español, Nederlands Suomi, Polski
Detailed information

Logo ERN: produced/endorsed by ERN(s) Logo FSMR: produced/endorsed by FSMR(s)

General public
Article for general public
Svenska (2016) - Socialstyrelsen
Guidelines
Emergency guidelines
Français (2024.pdf) - Orphanet Urgences
Clinical practice guidelines
English (2015) - Hematology Am Soc Hematol Educ Program Logo ERN
Disease review articles
Review article
Français (2006.pdf) - Rev Praticien
Diagnostic Keys
Français (2024) - Les clés du diagnostic Logo FSMR
The documents contained in this website are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.