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Brain arteriovenous malformation

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Disease definition

Cerebral arteriovenous malformation (AVM) is a congenital malformative communication between the veins and the arteries in the brain in the form of a nidus, an anatomical structure composed of dilated and tangled supplying arterioles and drainage veins with no intervening capillary bed, that can be asymptomatic or cause, depending on the location and the size of the AVM, headaches of varying severity, generalized or focal seizures, focalneurological defects (weakness, numbness, speech difficulties, vision loss) or potentially fatal intracranial hemorrhage in case the AVM ruptures.

ORPHA:46724

Classification level: Disorder

Synonym(s):
  • Cerebral arteriovenous malformation

Source: PubMed ID 36070978 33501562

Prevalence: 1-9 / 100 000

Inheritance: No data available

Age of onset: All ages

ICD-10: Q28.2

ICD-11: 8B22.40

OMIM: 108010

UMLS: C0917804

MeSH: D002538

GARD: 3020

MedDRA: 10056371

A summary on this disease is available in Français, Español, Italiano, Nederlands Suomi, Ελληνικά
Detailed information

Logo ERN: produced/endorsed by ERN(s) Logo FSMR: produced/endorsed by FSMR(s)

Guidelines
Emergency guidelines
Français (2018.pdf) - Orphanet Urgences
Clinical practice guidelines
The documents contained in this website are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.