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MAGIC syndrome

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Disease definition

A rare autoinflammatory syndrome characterized by the presence of features of relapsing polychondritis and Behçet's disease in the same individual. This includes cartilage inflammation of the ears, nose, throat, and rib cage, as well as recurrent oral and genital ulcers, respectively. Patients may also present ocular involvement (in particular anterior uveitis or scleritis), arthritis, fever, colitis, thrombophlebitis, central nervous system vasculitis, or, in rare cases, arterial aneurysms. Symptoms of polychondritis occur secondary to those of Behçet's disease in the vast majority of cases.

ORPHA:324972

Classification level: Disorder

Synonym(s):
  • Mouth and genital ulcers-inflamed cartilage syndrome

Prevalence: <1 / 1 000 000

Inheritance: -

Age of onset: Adolescent, Adult, Childhood

ICD-10: D89.8

UMLS: C0406568

GARD: 13371

MedDRA: 10078132

A summary on this disease is available in Français, Español, Deutsch, Italiano, Nederlands
Detailed information

Logo ERN: produced/endorsed by ERN(s) Logo FSMR: produced/endorsed by FSMR(s)

Guidelines
Emergency guidelines
Français (2019.pdf) - Orphanet Urgences
Clinical practice guidelines
English (2024) - J Clin Immunol Logo ERN
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