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Sandhoff disease, juvenile form

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ORPHA:309162

Classification level: Subtype of disorder

Synonym(s):
  • Beta-hexosaminidase subunit beta deficiency, juvenile form
  • GM2 gangliosidosis, Sandhoff variant, juvenile form
  • GM2 gangliosidosis, hexosaminidase A and B deficiency variant, juvenile form

Prevalence: -

Inheritance: Autosomal recessive

Age of onset: Adolescent, Childhood

ICD-10: E75.0

ICD-11: 5C56.00

OMIM: 268800

UMLS: C0751491

Summary

This disease is described under Sandhoff disease

Detailed information

Logo ERN: produced/endorsed by ERN(s) Logo FSMR: produced/endorsed by FSMR(s)

General public
Article for general public
Svenska (2024) - Socialstyrelsen
Guidelines
Emergency guidelines
Français (2013.pdf) - Orphanet Urgences
Clinical practice guidelines
Disease review articles
Clinical genetics review
English (2022) - GeneReviews
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