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Inherited isolated arrhythmogenic cardiomyopathy, dominant-right variant

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ORPHA:293910

Classification level: Subtype of disorder

Synonym(s):
  • Arrhythmogenic cardiomyopathy dominant-right variant
  • Arrhythmogenic cardiomyopathy with right ventricular involvement
  • Familial isolated arrhytmogenic ventricular dysplasia, right dominant form

Source: PubMed ID 32561223

Prevalence: -

Inheritance: Autosomal dominant

Age of onset:

ICD-10: I42.8

ICD-11: BC43.6

OMIM: 618920 600996 615616 610193 107970

UMLS: C5925015

Summary

This disease is described under Inherited isolated arrhythmogenic cardiomyopathy

Detailed information

Logo ERN: produced/endorsed by ERN(s) Logo FSMR: produced/endorsed by FSMR(s)

Guidelines
Emergency guidelines
Français (2019.pdf) - Orphanet Urgences
Clinical practice guidelines
English (2020) - Circulation Logo ERN
English (2019) - Heart Rhythm Logo ERN
Disease review articles
Review article
English (2016) - Orphanet J Rare Dis
Clinical genetics review
English (2023) - GeneReviews
Genetic testing
Guidance for genetic testing
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