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Alopecia antibody deficiency

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Disease definition

A rare primary immunodeficiency disorder characterized by the association of alopecia areata totalis and antibody deficiency (congenital agammaglobulinemia or incomplete antibody deficiency syndrome), manifesting with recurrent infections. There have been no further descriptions in the literature since 1976.

ORPHA:1006

Classification level: Disorder

Synonym(s):
  • Ipp-Gelfand syndrome

Source: PubMed ID 978318

Prevalence: <1 / 1 000 000

Inheritance: Unknown

Age of onset: Childhood, Infancy

ICD-10: D80.8

UMLS: C5190867

A summary on this disease is available in Français, Español, Deutsch, Italiano, Nederlands, Polski
Detailed information

Logo ERN: produced/endorsed by ERN(s) Logo FSMR: produced/endorsed by FSMR(s)

Guidelines
Emergency guidelines
Français (2020.pdf) - Orphanet Urgences
Clinical practice guidelines
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